Cystic fibrosis: diagnosis and management [NG78]

New Guidance from NICE:

This guideline covers diagnosing and managing cystic fibrosis.  It specifies how to monitor the condition and manage the symptoms to improve quality of life. There are also detailed recommendations on treating the most common infections in people with cystic fibrosis.

This guideline includes recommendations on:

• diagnosis
• service delivery, including how to organise services and multidisciplinary teams
• annual and routine reviews
• monitoring, assessment and management, including for lung disease, pulmonary infection, distal intestinal obstruction syndrome, liver disease and cystic-fibrosis-related diabetes
• preventing cross-infection

Equipment specification: cystic fibrosis and congenital hypothyroidism screening

Analytical equipment specification for the screening of cystic fibrosis (CF) and congenital hypothyroidism (CHT) for the newborn blood spot screening programme.

Fizzyo wins top tech health award

A physiotherapy-inspired computer gaming project for people with cystic fibrosis was chosen out of about 200 entries as the winner of the AbilityNet Tech4Good digital health award.

The idea behind the Fizzyo project is simple: to make physiotherapy breathing exercises fun – and encourage people to do them. It puts a wireless sensor into the mouthpiece of a conventional airway clearance device. As the user exhales, the sensor sends electronic signals that control computer games.

Physios join Microsoft for ground breaking cystic fibrosis tech project

A university physiotherapy department is working with Microsoft to develop computer games that motivate children with cystic fibrosis (CF) to complete breathing exercises to clear their lungs.

Non-cystic fibrosis bronchiectasis: inhaled tobramycin

This evidence summary includes 3 randomised controlled trials that investigated the efficacy of nebulised tobramycin, 300 mg twice daily compared with placebo for treating infective exacerbations caused by P aeruginosa in people with non-cystic fibrosis bronchiectasis. The treatment duration varied across the studies from 4 weeks to 6 months.